BChesser_Cystic Fibrosis_02042024

6 things about

Cystic Fibrosis

Risk Factors:

• Genetics ( It is caused by a mutations in a gene called the cystic fibrosis transmembrane conductance regulator.

• Nursing care strategies:
• Providing adequate nutrition. (Patient needs protien to help heal.
• Weight management. ( Makes sure the patient is not retaining fluid.)
• Adherence to medication regimen. (Educated on the importance of medication management and their purpose.
• Prevention of infection. (Monitor vital signs and encourage fluids.)
• Pulmonary hygiene. (Deep breathing and coughing to remove mucus from lungs.)

Treatment Team:

• Respiratory Nurse ( Neb treatments, High-frequency chest wall oscillation.)
• Main Provider (Monitors patient.)
• Pulmonologist ( Diagnosis /Monitors disease/ prescribe medication)
• Nurse ( Carries out orders.)
• Speech Therapy (Assist with breathing exercises.)
• Case Management (Helps set up appointments, medication, therapies
• Dietitian ( Provide adequate nutrition to the patient.)

References:Karakashian,A.L., & Schub, T. (2018) Cysti Fibrosis.CINHAL Nursing Guide. Retrieved From http://ezproxy.rasmussen.edu/login?url=https://search.ebscohost.com/login.aspx?direct=true& db=nup&AN=T700390^site-eds-live

Treatment:

• Oxygen therapy (It helps the patient with cirulation.)
• Lung Transplant ( The lung was so damaged they need a new one.)
• Postive expiratory pressure. ( Provides back pressure to the airways during expiration.)
• Chest Physiotherapy (Help break down the mucus.)

Resources:

• Children Hospital of Southwest Florida
• Joe DiMaggio Cystic Fibrosis. (Adults)
• All Children Hospital